Note modifica modifica wikitesto padilla w, newton hb, barbosa s, weber s syndrome and sixth nerve palsy secondary to decompression illness. This is the first case of penetrating brain injury with associated weber. Sturgeweber syndrome sws, or encephalotrigeminal angiomatosis, is a rare, congenital neurocutaneous syndrome characterized by unilateral facial cutaneous vascular malformation nevus. Note modifica modifica wikitesto padilla w, newton hb, barbosa s, webers syndrome and sixth nerve palsy secondary to decompression illness.
Sws is primarily marked by a facial capillary malformation portwine birthmark in the v1 distribution forehead andor eyelid of the facial region. Webers syndrome is one of the brainstem lesion syndromes. Seizures may worsen any associated cortical hypo perfusion with the potential to further impair both neurological and developmental delay. E causata da infarto mesencefalico a seguito di occlusione dei rami paramediani dellarteria.
Sturgeweber syndrome, include septal defects, valvular anomlies, transposition of the great vessels, aortic coarctation and rarely deep arteriovenous malformations. Wikimedia commons contiene immagini o altri file su sindrome di weber. Sturgeweber syndrome sws is a rare, congenital condition involving the brain, skin, and eye. Assieme alla sindrome di weber, alla sindrome dellarteria cerebellare superiore, alla sindrome di benedikt, alla sindrome di nielsen e alla sindrome di nothnagel fa parte delle sindromi alterne del mesencefalo. Weber syndrome due to penetrating wound in midbrain medigraphic. First described by schirmer and later more specifically by. Mesencefalo ventral, haz corticoespinal del 18 jul 2010 sindromes alternos del tallo. Weber, foi descrita primeiramente por schirmer 1860 e posteriormente especificada por sturge 1879 e complementada por weber 1922. Serra valdes 1 melissa serra ruiz 2 rafael comas valdespino 1. It is a dominant autosomic transmission determining multisystemic vascular dysplasia, which has been mapped to two genes, hht1 and hht2, determined by. Non e correlata alla sindrome di sturge weber o alla sindrome di klippeltrenaunay. Users can purchase an ebook on diskette or cd, but the most popular method of getting an ebook is to purchase a downloadable file of the ebook or other reading material from a web site such as barnes and noble to be read from the users computer or reading device. Sturgewebersyndrom hamartome, ektoneurodermale neuroektodermaldysplasie, kongenitale neurokutanes syndrom neuroretinoangiomatose phakomatose, sturgeweber angiomatosis encephalofacialis. A skt acomete invariavelmente os membros superiores e.
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